Juvenil Behçet’s Disease

Behçet disease is a vasculitis in which multiple organ involvement occurs. Remisions and exacerbations are seen in its course and it is a chronic relapsing disease. Diagnosis is very difficult. There are no patognomonic symptoms or laboratory signs. Recurent oral and genital ulserations, ocular and dermatological signs are diagnostic. The disease is rarely seen in childhood and sometimes presantation may be papilledema.

A ten year old were taken to our clinic because of headache, fatigue, cranial sinus thrombosis. No cause was found while searching all cranial occlusive causes of venous thrombosis emesis, myalgia sixteen months ago. When the etiology of headache searched papilledema was found as a result of. Diazoxide, low dose asetylsalisylate, warfarin were administered to the patient for cranial sagittal sinus right transverse sinus
thrombosis. MRI-MRI venograpy were used fo controlling sinus thrombosis.

Long term observation of the patient in the policlinic and in the hospital it is found that except the complaints of severe headache, relapsing fever, there are recurent oral ulcerations, non-erovise artritis of knee and lower extremities, erithema nodosume like dermal lesions in lower extremities, thrombophylebitis and iridocyclitis as the other signes. In addition to this, acute phase reactants were high during these periods. HLA B51 was found in his tissue group analyse. After labarotory data and clinical findings the patients diagnosis is juvenil Behçet’s disease. In our clinic his theraphy and visits are regularly controlled.

Jüvenil Behçet Hastalýðý