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Caroli’s disease: A case report [Medeniyet Med J]
Medeniyet Med J. 2009; 24(2): 92-94

Caroli’s disease: A case report

Ali Karaman1, Doğan Nasır Binici2, İhsan Doru3
1Erzurum Nenehatun Maternity Hospital, Genetics Unit, Erzurum
2Erzurum Nenehatun Maternity Hospital, Internal Medicine Clinic, Erzurum
3Erzurum Regional Training and Research Hospital, Radiology Unit, Erzurum

Caroli’s disease is a rare congenital disorder characterized by cytic dilatation of the intrahepatic bile ducts. Caroli’s disease is transmitted in autosomal recessive fashion. Chollangitis, liver cirrhosis, and cholangiocarcinoma are its potantial complications. The magnetic resonance cholangiography (MRCG) is the metod with the highest sensitivity in the diagnosis of Caroli’s disease. In this study, we present a case of a fifty year old grill who was diagnosid with Caroli’s disease (Caroli type I).

Keywords: Liver, biliary tract, cystic disease, caroli’s disease


Caroli hastalığı: Bir olgu sunumu

Ali Karaman1, Doğan Nasır Binici2, İhsan Doru3
1Erzurum Nenehatun Kadın Doğum Hastanesi, Genetik Ünitesi, Erzurum
2Erzurum Nenehatun Kadın Doğum Hastanesi, İç hastalıkları Kliniği, Erzurum
3Erzurum Bölge Eğitim ve Araştırma Hastanesi, Radyoloji Ünitesi, Erzurum

Anahtar Kelimeler: Karaciğer, safra yolları, kistik hastalık, caroli hastalığı


Ali Karaman, Doğan Nasır Binici, İhsan Doru. Caroli’s disease: A case report. Medeniyet Med J. 2009; 24(2): 92-94

Corresponding Author: Ali Karaman, Türkiye


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