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Two patients with DYKE-Davidoff-Masson syndrome [Medeniyet Med J]
Medeniyet Med J. 2012; 27(2): 72-76 | DOI: 10.5222/J.GOZTEPETRH.2012.072  

Two patients with DYKE-Davidoff-Masson syndrome

Fatma Candan, Sevda Gökçeer, Nihal Işık, Fatma Akyan, İlknur Aydın Cantürk, Semra Arı
T.C.S.B. Istanbul Goztepe Training and Research Hospital, Neurology Clinic, Istanbul

In this study, two patients with cerebral hemiatrophy, contralateral hemiparesia, hyperpneumatisation of synisus and drug resistant epileptic seizures were diagnosed as having Dyke- Davidoff-Mason Syndrome (DDMS) and both patients were evaluated as for clinical, radiological and etiological aspects of the disease and the responses to the treatment were determined.

Keywords: Dyke Davidoff Mason Syndrome, DDMS, drug resistant seizure disorder, hyperpneumatisation of sinuses, hemiparesia, cerebral hemiatrophy


DYKE-Davidoff-Masson sendromu ile iki olgu

Fatma Candan, Sevda Gökçeer, Nihal Işık, Fatma Akyan, İlknur Aydın Cantürk, Semra Arı
T.C.S.B. İstanbul Göztepe Eğitim ve Araştırma Hastanesi Nöroloji Kliniği, İstanbul

Bu çalışmada dirençli konvülziyon, serebral hemiatrofi, kontralateral hemiparezi, sinüslerde hiperpnömatizasyon ve dirençli nöbet nedeniyle takip ettiğimiz Dyke- Davidoff-Mason Sendromu (DDMS) tanısı konan iki hasta etiyoloji, klinik, radyolojik özellik ve tedavi açısından gözden geçirildi.

Anahtar Kelimeler: Dyke-Davidoff-Mason Syndrome, DDMS, ilaca dirençli epileptik hastalık, sinüslerde hiperpnömatizasyon, hemiparezi, serebral hemiatrofi


Fatma Candan, Sevda Gökçeer, Nihal Işık, Fatma Akyan, İlknur Aydın Cantürk, Semra Arı. Two patients with DYKE-Davidoff-Masson syndrome. Medeniyet Med J. 2012; 27(2): 72-76

Corresponding Author: Fatma Candan, Türkiye


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