Moya Moya syndrome

Moya moya syndrome (MMS) is a rare cerebrovascular disorder caused by segmentary stenosis and occlusions of the small vessels around the circle of Willis and distal branches of carotid arteries. The name of “moyamoya” means “puff of smoke” in Japanese and describes the look of the tangle of tiny vessels formed to compensate for the blockage. This disorder may presented transient paresis, headache, epilepsy, dementia, aphasia, ataxia and subarachnoid hemorrhage. Although MMS is considered a disease of unknown etiology, infectious and genetic causes have been blamed. In this article, we described a 48 year-old woman who diagnosed as MMS after investigation for etiology of transient ischeamic attacks and epileptic seizure. Also, clinical and radiological findings of this case are discussed in the light of the literature.

Moya Moya sendromu