Two cases of Infantile myofibromatosis: Multiple visceral involvement and a solitary soft tissue massMemduh Dursun1, Ensar Yekeler1, Hüseyin Kılınçaslan2, Abdulkadir Tepeler2, Fikri Demir3, Mehtap Tunacı1, Gülden Acunaş11Istanbul University Faculty of Medicine, Radiology, Istanbul
2Istanbul University Faculty of Medicine, Children's Surgery, Istanbul
3Istanbul University Faculty of Medicine, Child Health and Diseases, Istanbul
Infantile myofibromatosis is a rare myofibroblastic tumor in which soft tissue, bone and rarily visceral involvement can be seen. It is usually a solitary tumor, however, multicentric
involvement may also be present. The cases with solitary or multiple lesions but no visceral involvement have good prognosis and spontaneous regression can often be seen. Nevertheless, multicentric visceral tumors are associated with high mortality.
In this report, imaging findings of a case of infantile myofibromatosis with liver and both adrenal glands involvement; and another case with involvement of posterior thoracal and
servical region muscles are presented. Keywords: Infantil myofibromatosis, visceral and muscle involvement
İki infantil myofibromatozis olgusu: Multipl iç organ tutulumu, soliter yumuşak doku kitlesiMemduh Dursun1, Ensar Yekeler1, Hüseyin Kılınçaslan2, Abdulkadir Tepeler2, Fikri Demir3, Mehtap Tunacı1, Gülden Acunaş11İstanbul Üniversitesi İstanbul Tıp Fakültesi, Radyoloji ABD, İstanbul
2İstanbul Üniversitesi İstanbul Tıp Fakültesi, Çocuk Cerrahisi ABD, İstanbul
3İstanbul Üniversitesi İstanbul Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları ABD, İstanbul
Anahtar Kelimeler: İnfantil myofibromatozis, iç organ ve kas tutulumu
Memduh Dursun, Ensar Yekeler, Hüseyin Kılınçaslan, Abdulkadir Tepeler, Fikri Demir, Mehtap Tunacı, Gülden Acunaş. Two cases of Infantile myofibromatosis: Multiple visceral involvement and a solitary soft tissue mass. Medeniyet Med J. 2005; 20(2): 120-122
Corresponding Author: Memduh Dursun, Türkiye |
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