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Volume : 39 Issue : 1 Year : 2024



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Cystic Fibrosis Presenting as a Pseudo-Bartter’s Syndrome [Medeniyet Med J]
Medeniyet Med J. 2003; 18(4): 243-244

Cystic Fibrosis Presenting as a Pseudo-Bartter’s Syndrome

Neslihan Özkul Sağlam, Fatma Dursun, Atiye Fedakar, Metin Dönmez, Müferet Ergüven
Göztepe SSK Hospital, Children Clinic, Istanbul

Bartter syndrome are characterized by normal blood pressure, hypokalemia, metabolic alkalosis, prostaglandinuria, hyperreninemia and hyperaldosteronism and defined as a
family of inherited recessive autosomal tubulopathies. Pseudo-Bartter’s syndrome may produce a hypokalemic metabolic alkalosis without primary renal disease. The underlying
illnesses are primary hyperaldosteronism, Cushing syndrome, hypertrophic pyloric stenosis, cystic fibrosis and some drogs. In this article a 3 mounts old boy who diagnosed cystic fibrosis presenting as a pseudo-Bartter’s syndrome was evaluated.

Keywords: Metabolic alkalosis, pseudo-Bartter syndrome, cystic fibrosis


Pseudo-Bartter Sendromu Bulguları ile Ortaya Çıkan Bir Kistik Fibroz

Neslihan Özkul Sağlam, Fatma Dursun, Atiye Fedakar, Metin Dönmez, Müferet Ergüven
Göztepe SSK Eğitim Hastanesi, Çocuk Kliniği, İstanbul

Anahtar Kelimeler: Metabolik alkaloz, pseudo-Bartter sendromu, kistik fibrozis


Neslihan Özkul Sağlam, Fatma Dursun, Atiye Fedakar, Metin Dönmez, Müferet Ergüven. Cystic Fibrosis Presenting as a Pseudo-Bartter’s Syndrome. Medeniyet Med J. 2003; 18(4): 243-244

Corresponding Author: Neslihan Özkul Sağlam, Türkiye


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